Yavuz, İzzetBaşkan, ZelalÜlkü, RefikDülgergil, Türksel C.Darı, OsmanEce, AydınDarı, Kadriye Oya2020-06-252020-06-252006closedAccess0188-44091873-5487https://doi.org/10.1016/j.arcmed.2005.06.016https://hdl.handle.net/20.500.12587/3592yavuz, izzet/0000-0001-6953-747X; ECE, AYDIN/0000-0001-9130-2431; Ece, Aydin/0000-0001-6764-8336The aim of this article is to review possible cranio-maxillofacial deformative consequences associated with hypohidrotic ectodermal dysplasia and embryonic malformations, which include dental ageneses, and describe the oral habilitation. Hypohidrotic ectodermal dysplasia patients had a clinical examination and underwent radiographic and Steiner's analyses and a respiratory capability test before assessment and treatment. Fifteen patients (eight males and seven females, aged 5-45 years) had tooth ageneses (from hypodontia to anodontia) associated with cutaneous dyshydrosis and hair and nail dystrophy. Most patients had sparse or absent hair, a short face with an unusual facial concavity, a maxillary retrusion and a relative mandibular protrusion. Dentists must conduct a comprehensive and multidisciplinary approach to these patients in order to improve their dental, masticatory, growth and orthognathic conditions. (c) 2006 IMSS. Published by Elsevier Inc.eninfo:eu-repo/semantics/closedAccesshypohidrotic ectodermal dysplasiasdenturetooth agenesesArticle37340340910.1016/j.arcmed.2005.06.0162-s2.0-3364451928116513494Q1WOS:000236184900019Q3